|
Patient
|
Controls mean ± SD [range] (n = 29)
|
---|
Complex I/CS
|
0.06
|
0.34 ± 0.09 [0.18–0.58]
|
Complex II/CS
|
0.35
|
0.39 ± 0.07 [0.32–0.62]
|
Complex III/CS
|
0.51
|
1.20 ± 0.21 [0.75–1.71]
|
Complex IV/CS
|
1.2
|
3.8 ± 0.7 [2.5–5.7]
|
CS
|
634
|
309 ± 83 [181–468]
|
- Enzyme activity is expressed as milliunits per milliunits citrate synthase (CS). CS activity is expressed as milliunits per milligrams protein. Reference values are from 29 age-matched controls and expressed as mean ± SD with ranges in brackets