Major Criteria |
1. Beighton score of 4/9 or greater |
2. Arthralgia for more than 3 months in 4 or more joints |
Minor Criteria |
1. A Beighton score of 1, 2 or 3/9 (0 to 3 if over age 50) |
2. Arthralgia for more than 3 months in 1–3 joints, or back pain ≥3 months, or spondylosis, spondylolysis, spondylolisthesis |
3. Dislocation or subluxation in more than one joint, or in one joint on more than one occasion |
4. Soft tissue rheumatism in 3 or more locations (eg, epicondylitis, tenosynovitis, bursitis) |
5. Marfanoid habitus |
6. Abnormal skin (eg, striae, hyperextensible, thin, or papyraceous scarring) |
7. Eye abnormalities (eg, drooping eyelids, myopia, anti mongoloid slant) |
8. Varicose veins or hernia or uterine/rectal prolapse |
JHS is diagnosed in three cases, if present: I) Two major criteria; II) One major and two minor criteria; III) Four minor criteria. The disorder is excluded in those patients with MFS or EDS. |