From: Cervical rotation, chest deformity and pelvic obliquity in patients with spinal muscular atrophy
SMA I N = 21 | SMA II N = 36 | SMA III N = 17 | Control N = 89 | |
---|---|---|---|---|
Age (years) ± SD | 6.5 ± 5.0 | 7.4. ± 4.1 | 7.2 ± 4.0 | 6.8 ± 3.7 |
Weight (kg) ± SD | 20.7 ± 11.1 | 23.7 ± 10.6 | 21.6 ± 10.3 | 26.0 ± 13.4 |
Height (cm) ± SD | 116.6 ± 22.9 | 122.3 ± 17.9 | 121.1 ± 18.9 | 125.1 ± 23.4 |
CR left (o) ± SD | 20.4 ± 10.7 | 22.5 ± 9.1 | 24.5 ± 9.4 | 29.9 ± 4.8 |
Min / Max | 0.0 / 40.0 | 0.0 / 36.0 | 6.0 / 38.0 | 18.0 / 40.0 |
CR right (o) ± SD | 21.9 ± 10.8 | 24.8 ± 8.3 | 23.9 ± 9.3 | 30.4 ± 4.8 |
Min / Max | 2.0 / 44.0 | 5.0 / 40.0 | 6.0 / 38.0 | 20.0 / 42.0 |
CRS (o) ± SD | 42.3 ± 14.4 | 47.3 ± 14.3 | 48.4 ± 17.4 | 60.3 ± 9.3 |
Min / Max | 10.0 / 70.0 | 5.0 / 76.0 | 12.0 / 70.0 | 40.0 / 82.0 |
CRD (o) ± SD | 11.7 ± 10.7 | 6.9 ± 7.6 | 4.6 ± 4.6 | 2.0 ± 1.9 |
Min / Max | 0.0 / 38.0 | 0.0 / 32.0 | 0.0 / 11.0 | 0.0 / 8.0 |
SATRU (o) ± SD | 6.3 ± 3.8 | 4.3 ± 4.2 | 2.4 ± 1.7 | 0.5 ± 0.9 |
Min / Max | 0.0 / 14.0 | 0.0 / 15.0 | 0.0 / 5.0 | 0.0 / 3.0 |
SATRL (o) ± SD | 5.6 ± 3.7 | 5.1 ± 4.0 | 2.7 ± 1.8 | 0.3 ± 0.6 |
Min / Max | 0.0 / 15.0 | 0.0 / 15.0 | 0.0 / 7.0 | 0.0 / 3.0 |
PO (o) ± SD | NA | 8.7 ± 6.4 | 3.6 ± 3.0 | 0.8 ± 1.0 |
Min / Max | NA | 0.0 / 24.0 | 0.0 / 10.0 | 0.0 / 4.0 |
Single scoliosis Cobb angle (o) | ThL 32.2 ± 19.1 N = 17 | ThL 33.5 ± 15.0 N = 25 | ThL 29.0 ± 15.0 N = 8 | no scoliosis |
Double scoliosis Cobb angle (o) | Th 59.0 ± 4.2 ThL 51.0 ± 29.1 N = 2 | Th 43.4 ± 22.7 ThL 62.4 ± 26.5 N = 5 | no scoliosis | no scoliosis |