Table 1 Clinical Characteristics at Baseline for 40 Adult CF Patients

Age (years)

28.7 [8.4]

19–52

40

Age at first menstruation (years)

12.9 [1.5]

11–16

17

Height (cm)

166.4 [8.4]

150–183

38

Weight (kg)

57.4 [8.0]

43.3–78

38

Body mass index (gm / kg²)

20.6 [2.3]

16.6–25.1

37

VO₂max (L / min)¹

1.7 [0.6]

0.65–2.65

37

VO₂max (% normal)

87.9 [23.4]

37–117

37

FEV₁ (L)²

1.9 [0.6]

0.7–3.3

37

FEV₁ (% normal)

52.3 [15.7]

22–87

37

DLCO (mL / min / mmHg)³

19.8 [6.5]

2.05–34.2

37

DLCO (% normal)

60.0 [11.6]

40–85

37

Exercise capacity (kpm)⁴

797.3 [237.4]

400–1300

37

Exercise capacity (% normal)

76.6 [20.4]

41–113

37

Genotype

-

-

   homozygous Δ F508

12

   heterozygous Δ F508

18

   other heterozygous

5

   unknown

5